Cystic Fibrosis Research Today is a free monthly online journal that collates and summarizes the latest research about Cystic Fibrosis, including details on symptoms, genetics, treatment, information.

Volume 6 (2009), Issue 7 (July)

1. Pseudomonas aeruginosa microevolution during cystic fibrosis lung infection establishes clones with adapted virulence.
   Am J Respir Crit Care Med, 180(2): 138-45. [Abstract] [Full-text]
2. Human neutrophil peptides and phagocytic deficiency in bronchiectatic lungs.
   Am J Respir Crit Care Med, 180(2): 159-66. [Abstract] [Full-text]
3. Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening.
   Am J Respir Crit Care Med, 180(2): 146-52. [Abstract] [Full-text]
4. Effect of systemic inflammation on inspiratory and limb muscle strength and bulk in cystic fibrosis.
   Am J Respir Crit Care Med, 180(2): 153-8. [Abstract] [Full-text]
5. Recombinant activated factor VII for massive hemoptysis in patients with cystic fibrosis.
   Chest, 136(1): 277-81. [Abstract] [Full-text]
6. Multiple genotypic changes in hypersusceptible strains of Pseudomonas aeruginosa isolated from cystic fibrosis patients do not always correlate with the phenotype.
   J Antimicrob Chemother, 64(2): 294-300. [Abstract] [Full-text]
7. Dynasore inhibits removal of wild-type and DeltaF508 cystic fibrosis transmembrane conductance regulator (CFTR) from the plasma membrane.
   Biochem J, 421(3): 377-85. [Abstract] [Full-text]
8. Molecular Characterization of Stenotrophomonas maltophilia isolates from cystic fibrosis patients and the hospital environment.
   Infect Control Hosp Epidemiol, 30(8): 753-8. [Abstract] [Full-text]
9. Non-viral vectors in cystic fibrosis gene therapy: recent developments and future prospects.
   Expert Opin Biol Ther, 9(8): 991-1003. [Abstract] [Full-text]
10. Distal intestinal obstruction syndrome (DIOS) in patients with cystic fibrosis after lung transplantation.
    J Gastrointest Surg, 13(8): 1448-53. [Abstract] [Full-text]
11. Azithromycin increases survival and reduces lung inflammation in cystic fibrosis mice.
    Inflamm Res, 58(8): 491-501. [Abstract] [Full-text]
12. Role of CFTR, Pseudomonas aeruginosa and Toll-like receptors in cystic fibrosis lung inflammation.
    Biochem Soc Trans, 37: 863-7. [Abstract] [Full-text]
13. Novel regulatory mechanisms for the CFTR gene.
    Biochem Soc Trans, 37: 843-8. [Abstract] [Full-text]
14. Macrorheology of cystic fibrosis, chronic obstructive pulmonary disease & normal sputum.
    Respir Res, 10: 63. [Abstract] [Full-text]
15. Structural study and conformational behavior of the two different lipopolysaccharide O-antigens produced by the cystic fibrosis pathogen Burkholderia multivorans.
    Chemistry, 15(29): 7156-66. [Abstract] [Full-text]
16. CFTR delivery to 25% of surface epithelial cells restores normal rates of mucus transport to human cystic fibrosis airway epithelium.
    PLoS Biol, 7(7): e1000155. [Abstract] [Full-text]
17. A cystic fibrosis respiratory epithelial cell chronically treated by miglustat acquires a non-cystic fibrosis-like phenotype.
    Am J Respir Cell Mol Biol, 41(2): 217-25. [Abstract] [Full-text]
18. Effects of azithromycin on glutathione S-transferases in cystic fibrosis airway cells.
    Am J Respir Cell Mol Biol, 41(2): 199-206. [Abstract] [Full-text]
19. Preconceptional ancestry-based carrier couple screening for cystic fibrosis and haemoglobinopathies: what determines the intention to participate or not and actual participation?
    Eur J Hum Genet, 17(8): 999-1009. [Abstract] [Full-text]
20. Treatment of acne with oral isotretinoin in patients with cystic fibrosis.
    Arch Dis Child, 94(8): 583-6. [Abstract] [Full-text]
21. Using a thoracic epidural catheter in a high-risk pediatric transplant patient.
    Ann Thorac Surg, 88(2): 654-6. [Abstract] [Full-text]
22. Effect of mutator P. aeruginosa on antibiotic resistance acquisition and respiratory function in cystic fibrosis.
    Pediatr Pulmonol, 44(8): 820-5. [Abstract] [Full-text]
23. Relations between depressive and anxious symptoms and quality of life in caregivers of children with cystic fibrosis.
    Pediatr Pulmonol, 44(8): 784-92. [Abstract] [Full-text]
24. Using index of ventilation to assess response to treatment for acute pulmonary exacerbation in children with cystic fibrosis.
    Pediatr Pulmonol, 44(8): 733-42. [Abstract] [Full-text]
25. Impact of hypochlorite-based disinfection on bacterial contamination of cystic fibrosis patients' home-nebulisers.
    J Hosp Infect, 72(4): 351-7. [Abstract] [Full-text]
26. Efficacy and tolerability of Creon for Children in infants and toddlers with pancreatic exocrine insufficiency caused by cystic fibrosis: an open-label, single-arm, multicenter study.
    Pancreas, 38(6): 693-9. [Abstract] [Full-text]
27. Proteomic identification of OprL as a seromarker for initial diagnosis of Pseudomonas aeruginosa infection of patients with cystic fibrosis.
    J Clin Microbiol, 47(8): 2483-8. [Abstract] [Full-text]
28. Cystic fibrosis transmembrane conductance regulator and caveolin-1 regulate epithelial cell internalization of Pseudomonas aeruginosa.
    Am J Physiol Cell Physiol, 297(2): C263-77. [Abstract] [Full-text]

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