Cystic Fibrosis Research Today is a free monthly online journal that collates and summarizes the latest research about Cystic Fibrosis, including details on symptoms, genetics, treatment, information.

Volume 4 (2007), Issue 4 (April)

1. Novel tobramycin inhalation powder in cystic fibrosis subjects: pharmacokinetics and safety.
   Pediatr Pulmonol, 42(4): 307-13. [Abstract] [Full-text]
2. Potential role of the cellular allergen stimulation test (CAST) in diagnosis of allergic bronchopulmonary aspergillosis (ABPA) in cystic fibrosis.
   Pediatr Pulmonol, 42(4): 314-8. [Abstract] [Full-text]
3. Protein kinase CK2, cystic fibrosis transmembrane conductance regulator, and the deltaF508 mutation: F508 deletion disrupts a kinase-binding site.
   J Biol Chem, 282(14): 10804-13. [Abstract] [Full-text]
4. Release of the antimicrobial peptide LL-37 from DNA/F-actin bundles in cystic fibrosis sputum.
   Eur Respir J, 29(4): 624-32. [Abstract] [Full-text]
5. Increased arylsulfatase B activity in cystic fibrosis cells following correction of CFTR.
   Clin Chim Acta, 380(1): 122-7. [Abstract] [Full-text]
6. MUC5AC and MUC5B mucins increase in cystic fibrosis airway secretions during pulmonary exacerbation.
   Am J Respir Crit Care Med, 175(8): 816-21. [Abstract] [Full-text]
7. Association between pulmonary function and sputum biomarkers in cystic fibrosis.
   Am J Respir Crit Care Med, 175(8): 822-8. [Abstract] [Full-text]
8. Intrinsic pro-angiogenic status of cystic fibrosis airway epithelial cells.
   Biochem Biophys Res Commun, 356(3): 745-9. [Abstract] [Full-text]
9. The expression of the mitochondrial gene MT-ND4 is downregulated in cystic fibrosis.
   Biochem Biophys Res Commun, 356(3): 805-9. [Abstract] [Full-text]
10. Nutritional management of cystic fibrosis patients.
    Curr Opin Clin Nutr Metab Care, 10(3): 348-54. [Abstract] [Full-text]
11. Economic implications of newborn screening for cystic fibrosis: a cost of illness retrospective cohort study.
    Lancet, 369(9568): 1187-95. [Abstract] [Full-text]
12. Cardiopulmonary bypass for lung transplantation in cystic fibrosis: pilot evaluation of perioperative outcome.
    J Cardiothorac Vasc Anesth, 21(2): 208-11. [Abstract] [Full-text]
13. Special considerations for patients with cystic fibrosis undergoing lung transplantation.
    Chest, 131(4): 1224-31. [Abstract] [Full-text]
14. Infection with Burkholderia cepacia complex bacteria and pulmonary exacerbations of cystic fibrosis.
    Chest, 131(4): 1188-96. [Abstract] [Full-text]
15. Effect of albuterol on maximal exercise capacity in cystic fibrosis.
    Chest, 131(4): 1181-7. [Abstract] [Full-text]
16. Proteomic biomarker discovery for the monogenic disease cystic fibrosis.
    Expert Rev Proteomics, 4(2): 199-209. [Abstract] [Full-text]
17. Prediction of cellular immune responses against CFTR in patients with cystic fibrosis after gene therapy.
    Am J Respir Cell Mol Biol, 36(5): 529-33. [Abstract] [Full-text]
18. MPB-07 reduces the inflammatory response to Pseudomonas aeruginosa in cystic fibrosis bronchial cells.
    Am J Respir Cell Mol Biol, 36(5): 615-24. [Abstract] [Full-text]
19. In vitro prediction of stop-codon suppression by intravenous gentamicin in patients with cystic fibrosis: a pilot study.
    BMC Med, 5: 5. [Abstract] [Full-text]
20. Chloride transporting capability of Calu-3 epithelia following persistent knockdown of the cystic fibrosis transmembrane conductance regulator, CFTR.
    Br J Pharmacol, 150(8): 1055-65. [Abstract] [Full-text]
21. ICAM-1 expression on conjunctival epithelial cells in patients with cystic fibrosis.
    Cytometry B Clin Cytom, 72(3): 204-8. [Abstract] [Full-text]
22. Differential effects of cyclic and constant stress on ATP release and mucociliary transport by human airway epithelia.
    J Physiol, 580: 577-92. [Abstract] [Full-text]
23. Inactivation of the mismatch repair system in Pseudomonas aeruginosa attenuates virulence but favors persistence of oropharyngeal colonization in cystic fibrosis mice.
    J Bacteriol, 189(9): 3665-8. [Abstract] [Full-text]
24. Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung disease.
    Cochrane Database Syst Rev. [Abstract] [Full-text]
25. Molecular epidemiology and dynamics of Pseudomonas aeruginosa populations in lungs of cystic fibrosis patients.
    Infect Immun, 75(5): 2214-24. [Abstract] [Full-text]
26. Detection of antibodies to Pseudomonas aeruginosa in serum and oral fluid from patients with cystic fibrosis.
    J Med Microbiol, 56: 670-4. [Abstract] [Full-text]
27. Computed tomography reflects lower airway inflammation and tracks changes in early cystic fibrosis.
    Am J Respir Crit Care Med, 175(9): 943-50. [Abstract] [Full-text]
28. Low bone mineral density in young children with cystic fibrosis.
    Am J Respir Crit Care Med, 175(9): 951-7. [Abstract] [Full-text]
29. An overview of monitoring and supplementation of omega 3 fatty acids in cystic fibrosis.
    Clin Biochem, 40(8): 511-20. [Abstract] [Full-text]
30. Autoantibody response to BPI predict disease severity and outcome in cystic fibrosis.
    J Cyst Fibros, 6(3): 228-33. [Abstract] [Full-text]
31. Partial Splenic Embolization: successful treatment of hypersplenism, secondary to biliary cirrhosis and portal hypertension in cystic fibrosis.
    J Cyst Fibros, 6(3): 212-4. [Abstract] [Full-text]
32. Work disability in adults with cystic fibrosis and its relationship to quality of life.
    J Cyst Fibros, 6(3): 223-7. [Abstract] [Full-text]
33. Reliability of multilocus sequence typing of the Burkholderia cepacia complex in cystic fibrosis.
    J Cyst Fibros, 6(3): 215-9. [Abstract] [Full-text]
34. N1303K and IVS8-5T, clinical presentation within a family with atypical cystic fibrosis.
    J Cyst Fibros, 6(3): 220-2. [Abstract] [Full-text]
35. Cystic fibrosis related diabetes in an extremely young patient.
    J Cyst Fibros, 6(3): 247-9. [Abstract] [Full-text]
36. Newborn screening for CF in a regional paediatric centre: the psychosocial effects of false-positive IRT results on parents.
    J Cyst Fibros, 6(3): 250-4. [Abstract] [Full-text]
37. Fosfomycin--investigation of a possible new route of administration of an old drug. A case study.
    J Cyst Fibros, 6(3): 244-6. [Abstract] [Full-text]
38. Coagulopathy in two patients with cystic fibrosis treated with ciprofloxacin.
    J Cyst Fibros, 6(3): 209-11. [Abstract] [Full-text]
39. A specific database for providing local and national level of integration of clinical data in cystic fibrosis.
    J Cyst Fibros, 6(3): 187-93. [Abstract] [Full-text]
40. Facial nerve palsy associated with a low serum vitamin A level in an infant with cystic fibrosis.
    J Cyst Fibros, 6(3): 241-3. [Abstract] [Full-text]
41. Restless leg syndrome manifested by iron deficiency from chronic hemoptysis in cystic fibrosis.
    J Cyst Fibros, 6(3): 234-6. [Abstract] [Full-text]
42. Use of continuous subcutaneous insulin infusion in patients with cystic fibrosis related diabetes: three case reports.
    J Cyst Fibros, 6(3): 237-40. [Abstract] [Full-text]
43. CFTR gene analysis in Latin American CF patients: heterogeneous origin and distribution of mutations across the continent.
    J Cyst Fibros, 6(3): 194-208. [Abstract] [Full-text]
44. Cystic fibrosis mortality trends in France.
    J Cyst Fibros, 6(3): 179-86. [Abstract] [Full-text]
45. Adherence of adult cystic fibrosis patients with airway clearance and exercise regimens.
    J Cyst Fibros, 6(3): 163-70. [Abstract] [Full-text]
46. Monitoring quality of life in outpatients with cystic fibrosis: feasibility and longitudinal results.
    J Cyst Fibros, 6(3): 171-8. [Abstract] [Full-text]
47. Pilot study of safety and tolerability of inhaled hypertonic saline in infants with cystic fibrosis.
    Pediatr Pulmonol, 42(5): 471-6. [Abstract] [Full-text]
48. Enhanced IL-1beta-induced IL-8 production in cystic fibrosis lung epithelial cells is dependent of both mitogen-activated protein kinases and NF-kappaB signaling.
    Biochem Biophys Res Commun, 357(2): 402-7. [Abstract] [Full-text]
49. Liver disease as risk factor for cystic fibrosis-related diabetes development.
    Acta Paediatr, 96(5): 736-9. [Abstract] [Full-text]
50. Current issues in quality improvement in cystic fibrosis.
    Clin Chest Med, 28(2): 459-72. [Abstract] [Full-text]
51. Advances in lung transplantation for patients who have cystic fibrosis.
    Clin Chest Med, 28(2): 445-57. [Abstract] [Full-text]
52. Fertility and pregnancy: common concerns of the aging cystic fibrosis population.
    Clin Chest Med, 28(2): 433-43. [Abstract] [Full-text]
53. Transition and transfer of patients who have cystic fibrosis to adult care.
    Clin Chest Med, 28(2): 423-32. [Abstract] [Full-text]
54. Imaging of the chest in cystic fibrosis.
    Clin Chest Med, 28(2): 405-21. [Abstract] [Full-text]
55. Infection control practice in cystic fibrosis centers.
    Clin Chest Med, 28(2): 381-404. [Abstract] [Full-text]
56. Novel therapies for the treatment of cystic fibrosis: new developments in gene and stem cell therapy.
    Clin Chest Med, 28(2): 361-79. [Abstract] [Full-text]
57. Macrolides in cystic fibrosis.
    Clin Chest Med, 28(2): 347-60. [Abstract] [Full-text]
58. Inflammation and anti-inflammatory therapies for cystic fibrosis.
    Clin Chest Med, 28(2): 331-46. [Abstract] [Full-text]
59. Nutrition and lung disease in cystic fibrosis.
    Clin Chest Med, 28(2): 319-30. [Abstract] [Full-text]
60. Approaches to the treatment of initial Pseudomonas aeruginosa infection in children who have cystic fibrosis.
    Clin Chest Med, 28(2): 307-18. [Abstract] [Full-text]
61. Newborn screening for cystic fibrosis.
    Clin Chest Med, 28(2): 297-305. [Abstract] [Full-text]
62. Pathogenesis of bronchiectasis.
    Clin Chest Med, 28(2): 289-96. [Abstract] [Full-text]
63. Cystic fibrosis: a review of epidemiology and pathobiology.
    Clin Chest Med, 28(2): 279-88. [Abstract] [Full-text]
64. Glucose homeostasis and genotype-phenotype interplay in cystic fibrosis patients with CFTR gene deltaF508 mutation.
    Diabetes Care, 30(5): 1187-92. [Abstract] [Full-text]
65. Microvascular complications in cystic fibrosis-related diabetes.
    Diabetes Care, 30(5): 1056-61. [Abstract] [Full-text]

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