Cystic Fibrosis Research Today is a free monthly online journal that collates and summarizes the latest research about Cystic Fibrosis, including details on symptoms, genetics, treatment, information.

Volume 2 (2005), Issue 3 (March)

1. Epidemiology of Pseudomonas aeruginosa in a cystic fibrosis rehabilitation centre.
   Eur Respir J, 25(3): 474-81. [Abstract] [Full-text]
2. The CFTR 3849+10kbC->T and 2789+5G->A alleles are associated with a mild CF phenotype.
   Eur Respir J, 25(3): 468-73. [Abstract] [Full-text]
3. Antimicrobial use and Pseudomonas aeruginosa susceptibility profile in a cystic fibrosis centre.
   Int J Antimicrob Agents, 25(3): 193-7. [Abstract] [Full-text]
4. Optimum peripheral drug deposition in patients with cystic fibrosis.
   J Aerosol Med, 18(1): 45-54. [Abstract] [Full-text]
5. Structural changes to airway smooth muscle in cystic fibrosis.
   Thorax, 60(3): 226-8. [Abstract] [Full-text]
6. Safety and tolerability of denufosol tetrasodium inhalation solution, a novel P2Y2 receptor agonist: results of a phase 1/phase 2 multicenter study in mild to moderate cystic fibrosis.
   Pediatr Pulmonol, 39(4): 339-48. [Abstract] [Full-text]
7. Misdiagnosing cystic fibrosis in the era of gene analysis: case reports.
   Pediatr Pulmonol, 39(4): 379-81. [Abstract] [Full-text]
8. Thrombophilia in children with cystic fibrosis.
   Pediatr Pulmonol, 39(4): 306-10. [Abstract] [Full-text]
9. Beyond chloride transport: CFTR in the 21st century-introductory remarks to a new state of the art series.
   Pediatr Pulmonol, 39(4): 289-91. [Abstract] [Full-text]
10. Insulin-secretion abnormalities and clinical deterioration related to impaired glucose tolerance in cystic fibrosis.
    Eur J Endocrinol, 152(2): 241-7. [Abstract] [Full-text]
11. Airway colonization by Acrophialophora fusispora in patients with cystic fibrosis.
    J Clin Microbiol, 43(3): 1484-7. [Abstract] [Full-text]
12. The impact of cystic fibrosis and PSTI/SPINK1 gene mutations on susceptibility to chronic pancreatitis.
    Clin Lab Med, 25(1): 79-100. [Abstract] [Full-text]
13. Salivary secretion assay for drug efficacy for cystic fibrosis in mice.
    Exp Physiol, 90(2): 189-93. [Abstract] [Full-text]
14. Rapidly progressive lung disease in a patient with cystic fibrosis on long-term azithromycin: possible role of mycoplasma infection.
    J Cyst Fibros, 4(1): 71-3. [Abstract] [Full-text]
15. A pilot study of oral L-arginine in cystic fibrosis.
    J Cyst Fibros, 4(1): 67-9. [Abstract] [Full-text]
16. Associations between clinical variables and quality of life in adults with cystic fibrosis.
    J Cyst Fibros, 4(1): 59-66. [Abstract] [Full-text]
17. Asians with cystic fibrosis in the UK have worse disease outcomes than clinic matched white homozygous delta F508 controls.
    J Cyst Fibros, 4(1): 53-8. [Abstract] [Full-text]
18. Risk factors for acquisition of methicillin-resistant Staphylococcus aureus (MRSA) by patients with cystic fibrosis.
    J Cyst Fibros, 4(1): 49-52. [Abstract] [Full-text]
19. Prospective evaluation of emerging bacteria in cystic fibrosis.
    J Cyst Fibros, 4(1): 41-8. [Abstract] [Full-text]
20. Long-term azitromycin treatment of cystic fibrosis patients with chronic Pseudomonas aeruginosa infection; an observational cohort study.
    J Cyst Fibros, 4(1): 35-40. [Abstract] [Full-text]
21. Late diagnosis defines a unique population of long-term survivors of cystic fibrosis.
    Am J Respir Crit Care Med, 171(6): 621-6. [Abstract] [Full-text]
22. Growth hormone treatment enhances nutrition and growth in children with cystic fibrosis receiving enteral nutrition.
    J Pediatr, 146(3): 324-8. [Abstract] [Full-text]
23. Guide to bone health and disease in cystic fibrosis.
    J Clin Endocrinol Metab, 90(3): 1888-96. [Abstract] [Full-text]
24. Uncertainty management following a positive newborn screening for cystic fibrosis.
    J Health Commun, 10(1): 57-76. [Abstract] [Full-text]
25. Cystic fibrosis airway epithelial Ca2+ i signaling: the mechanism for the larger agonist-mediated Ca2+ i signals in human cystic fibrosis airway epithelia.
    J Biol Chem, 280(11): 10202-9. [Abstract] [Full-text]
26. Fat absorption in cystic fibrosis mice is impeded by defective lipolysis and post-lipolytic events.
    Am J Physiol Gastrointest Liver Physiol, 288(4): G646-53. [Abstract] [Full-text]
27. Heat-stable enterotoxin of Escherichia coli stimulates a non-CFTR-mediated duodenal bicarbonate secretory pathway.
    Am J Physiol Gastrointest Liver Physiol, 288(4): G654-63. [Abstract] [Full-text]
28. Identification of N-acylhomoserine lactones in mucopurulent respiratory secretions from cystic fibrosis patients.
    FEMS Microbiol Lett, 244(2): 297-304. [Abstract] [Full-text]
29. Erythrocytes of humans with cystic fibrosis fail to stimulate nitric oxide synthesis in isolated rabbit lungs.
    Am J Physiol Heart Circ Physiol, 288(4): H1580-5. [Abstract] [Full-text]
30. Novel molecular approaches to cystic fibrosis gene therapy.
    Biochem J, 387: 1-15. [Abstract] [Full-text]
31. Increased prevalence of chronic rhinosinusitis in carriers of a cystic fibrosis mutation.
    Arch Otolaryngol Head Neck Surg, 131(3): 237-40. [Abstract] [Full-text]
32. Novel mouse model of chronic Pseudomonas aeruginosa lung infection mimicking cystic fibrosis.
    Infect Immun, 73(4): 2504-14. [Abstract] [Full-text]
33. Lack of association of common cystic fibrosis transmembrane conductance regulator gene mutations with primary sclerosing cholangitis.
    Am J Gastroenterol, 100(4): 874-8. [Abstract] [Full-text]
34. Cystic fibrosis prenatal screening in genetic counseling practice: recommendations of the National Society of Genetic Counselors.
    J Genet Couns, 14(1): 1-15. [Abstract] [Full-text]
35. A survey of sexual and reproductive health in men with cystic fibrosis: new challenges for adolescent and adult services.
    Thorax, 60(4): 326-30. [Abstract] [Full-text]
36. Association of tumour necrosis factor alpha variants with the CF pulmonary phenotype.
    Thorax, 60(4): 320-5. [Abstract] [Full-text]
37. Airway gene therapy and cystic fibrosis.
    J Paediatr Child Health, 41(3): 94-6. [Abstract] [Full-text]
38. Optical detection and discrimination of cystic fibrosis-related genetic mutations using oligonucleotide-nanoparticle conjugates.
    Anal Bioanal Chem, 381(6): 1122-9. [Abstract] [Full-text]
39. Bcl-2 sustains increased mucous and epithelial cell numbers in metaplastic airway epithelium.
    Am J Respir Crit Care Med, 171(7): 764-72. [Abstract] [Full-text]
40. The effect of varying tonicity on nasal epithelial ion transport in cystic fibrosis.
    Am J Respir Crit Care Med, 171(7): 760-3. [Abstract] [Full-text]
41. Assessment of nutritional status in adult patients with cystic fibrosis: whole-body bioimpedance vs body mass index, skinfolds, and leg-to-leg bioimpedance.
    J Am Diet Assoc, 105(4): 549-55. [Abstract] [Full-text]

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