Cystic Fibrosis Research Today is a free monthly online journal that collates and summarizes the latest research about Cystic Fibrosis, including details on symptoms, genetics, treatment, information.

Volume 2 (2005), Issue 2 (February)

1. Compacted DNA nanoparticles administered to the nasal mucosa of cystic fibrosis subjects are safe and demonstrate partial to complete cystic fibrosis transmembrane regulator reconstitution.
   Hum Gene Ther, 15(12): 1255-69. [Abstract] [Full-text]
2. Nontuberculous mycobacteria in cystic fibrosis associated with allergic bronchopulmonary aspergillosis and steroid therapy.
   Eur Respir J, 25(2): 324-8. [Abstract] [Full-text]
3. Long-term clearance from small airways in patients with cystic fibrosis.
   Eur Respir J, 25(2): 317-23. [Abstract] [Full-text]
4. Effect of cystic fibrosis exacerbations on neutrophil function.
   Int Immunopharmacol, 5(3): 601-8. [Abstract] [Full-text]
5. Longitudinal development of mucoid Pseudomonas aeruginosa infection and lung disease progression in children with cystic fibrosis.
   JAMA, 293(5): 581-8. [Abstract] [Full-text]
6. Reconstitution of O-specific lipopolysaccharide expression in Burkholderia cenocepacia strain J2315, which is associated with transmissible infections in patients with cystic fibrosis.
   J Bacteriol, 187(4): 1324-33. [Abstract] [Full-text]
7. Pancreatic enzyme therapy and clinical outcomes in patients with cystic fibrosis.
   J Pediatr, 146(2): 189-93. [Abstract] [Full-text]
8. Conductivity determined by a new sweat analyzer compared with chloride concentrations for the diagnosis of cystic fibrosis.
   J Pediatr, 146(2): 183-8. [Abstract] [Full-text]
9. The DeltaF508 cystic fibrosis mutation impairs domain-domain interactions and arrests post-translational folding of CFTR.
   Nat Struct Mol Biol, 12(1): 17-25. [Abstract] [Full-text]
10. Effects of liver transplantation on the nutritional status of patients with cystic fibrosis.
    Transpl Int, 18(2): 246-55. [Abstract] [Full-text]
11. Implementing prenatal screening for cystic fibrosis in routine obstetric practice.
    Am J Obstet Gynecol, 192(2): 527-34. [Abstract] [Full-text]
12. NF-kappaB activation and sustained IL-8 gene expression in primary cultures of cystic fibrosis airway epithelial cells stimulated with Pseudomonas aeruginosa.
    Am J Physiol Lung Cell Mol Physiol, 288(3): L471-9. [Abstract] [Full-text]
13. High heterogeneity of CFTR mutations and unexpected low incidence of cystic fibrosis in the Mediterranean France.
    J Cyst Fibros, 3(4): 265-72. [Abstract] [Full-text]
14. Genotype-phenotype relationship for five CFTR mutations frequently identified in western France.
    J Cyst Fibros, 3(4): 259-63. [Abstract] [Full-text]
15. Cellular proteolysis and systemic inflammation during exacerbation in cystic fibrosis.
    J Cyst Fibros, 3(4): 253-8. [Abstract] [Full-text]
16. Determination of tobramycin in saliva is not suitable for therapeutic drug monitoring of patients with cystic fibrosis.
    J Cyst Fibros, 3(4): 249-51. [Abstract] [Full-text]
17. Total body water in children with cystic fibrosis using bioelectrical impedance.
    J Cyst Fibros, 3(4): 243-7. [Abstract] [Full-text]
18. Sequential use of oxygen and bi-level ventilation for respiratory failure in cystic fibrosis.
    J Cyst Fibros, 3(4): 237-42. [Abstract] [Full-text]
19. Randomised double blind placebo controlled trial investigating the effect of calcium and vitamin D supplementation on bone mineral density and bone metabolism in adult patients with cystic fibrosis.
    J Cyst Fibros, 3(4): 233-6. [Abstract] [Full-text]
20. Cytokines and inflammatory mediators in cystic fibrosis.
    J Cyst Fibros, 3(4): 223-31. [Abstract] [Full-text]
21. Clinical importance of cystic fibrosis-related diabetes.
    J Cyst Fibros, 3(4): 209-22. [Abstract] [Full-text]
22. Circulating markers to assess nutritional therapy in cystic fibrosis.
    Clin Chim Acta, 353(1): 13-29. [Abstract] [Full-text]
23. Ventilation inhomogeneities in relation to standard lung function in patients with cystic fibrosis.
    Am J Respir Crit Care Med, 171(4): 371-8. [Abstract] [Full-text]
24. Bronchial constriction and inhaled colistin in cystic fibrosis.
    Chest, 127(2): 522-9. [Abstract] [Full-text]
25. Once versus three-times daily regimens of tobramycin treatment for pulmonary exacerbations of cystic fibrosis--the TOPIC study: a randomised controlled trial.
    Lancet, 365(9459): 573-8. [Abstract] [Full-text]
26. Development of a rapid colorimetric time-kill assay for determining the in vitro activity of ceftazidime and tobramycin in combination against Pseudomonas aeruginosa.
    J Microbiol Methods, 61(2): 171-9. [Abstract] [Full-text]
27. Weight and energy: parents' and children's perspectives on managing cystic fibrosis diet.
    Arch Dis Child, 90(3): 249-52. [Abstract] [Full-text]
28. A shortened adeno-associated virus expression cassette for CFTR gene transfer to cystic fibrosis airway epithelia.
    Proc Natl Acad Sci U S A, 102(8): 2952-7. [Abstract] [Full-text]
29. Phenotypic expression of genotype-phenotype correlation in cystic fibrosis patients carrying the 852del22 mutation.
    Am J Med Genet A, 132(4): 434-40. [Abstract] [Full-text]
30. Activities of Pseudomonas aeruginosa effectors secreted by the Type III secretion system in vitro and during infection.
    Infect Immun, 73(3): 1695-705. [Abstract] [Full-text]

© 2004-2008 Cystic Fibrosis Research Today. All Rights Reserved.